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Abstract
EXTRANODALMANIFESTATIONOFALK+ANAPLASTICLARGECELL
LYMPHOMAINCHILDREN:ACASEREPORT
Lymphomasrepresentaheterogenousgroupofhaematologicalmalignanciesoriginatingfrom
clonalproliferationoflymphocytes.Tumoursofthehematopoieticandlymphoidtissuesstand
togetherforahalfofallpaediatricmalignancies.Anaplasticlargecelllymphoma(ALCL)is
apleomorphicT-celllymphomacharacterisedbyCD30expression.ExpressionofAnaplastic
LymphomaKinase(ALK)dividesALCLintotwosubtypes:ALK-positive(withpredominance
inchildren),andALK-negative,mostlytobefoundinolderpatients.ALCLaccountsfor5%of
allnon-Hodgkinlymphomasandupto30%ofallchildhoodlymphomas.Wepresentaclinical
caseofa9-year-oldboyadmittedtoasurgicaldepartmentwithinflamedabscess-likesingleskin